a Contrast-enhanced computed tomography (CECT) portal phase (axial section at the level of portal vein bifurcation) showing hypertrophic left lateral (yellow) and medial (red) segments, hypertrophic caudate lobe (blue), and atrophic right lobe (green). LLS—left lateral segment, LMS—left medial segment, RL—right lobe, CL—caudate lobe. b Three-dimensional virtual liver segmentation showing hypertrophied left lobe (837cc) vs small right lobe (536cc). RL—right lobe, LL—left lobe. c Coronal section in CECT showing multiple cysts in bilateral kidneys. d T2-weighted magnetic resonance imaging showing high periportal signal intensities with widened portal tracts (red arrows).